Revised_natural_history_model_guideline v.1

A scoring system used to estimate survival from primary sclerosing cholangitis (PSC).

Maryam Razavi

maryam.razavi@cambio.se

Cambio CDS

To estimate survival from primary sclerosing cholangitis.

Use in patients with known primary sclerosing cholangitis.\nFormula:\nRisk Score = 0.03*(age [y]) + 0.54*loge(bilirubin [mg/dL]) + 0.54*loge(aspartate aminotransferase [U/L]) + 1.24*(variceal bleeding [Y=1,N=0]) - 0.84*(albumin [g/dL]

1. Kim WR, Therneau TM, Wiesner RH, Poterucha JJ, Benson JT, Malinchoc M, LaRusso NF, Lindor KD, Dickson ER. A revised natural history model for primary sclerosing cholangitis. Mayo Clin Proc. 2000 Jul;75(7):688-94. doi: 10.4065/75.7.688. PMID: 10907383. 2. Ponsioen CY, Vrouenraets SM, Prawirodirdjo W, Rajaram R, Rauws EA, Mulder CJ, Reitsma JB, Heisterkamp SH, Tytgat GN. Natural history of primary sclerosing cholangitis and prognostic value of cholangiography in a Dutch population. Gut. 2002 Oct;51(4):562-6. doi: 10.1136/gut.51.4.562. PMID: 12235081; PMCID: PMC1773389.

OBSERVATION.basic_demographic.v1, OBSERVATION.lab_test-bilirubin.v1, OBSERVATION.lab_test-ast.v1, OBSERVATION.revised_natural_history_model.v0, OBSERVATION.laboratory_test_result-serum_albumin.v1